Congenital portosystemic shunts: 2 cases report and review of literature

XU Jiaxin; DAI Liying; ZHANG Jian; WANG Juan; LIU Yu

doi:10.16766/j.cnki.issn.1674-4152.003316

Volume 21 Issue 12

Dec. 2023

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Article Navigation > Chinese Journal of General Practice > 2023 > 21(12): 2173-2176

XU Jiaxin, DAI Liying, ZHANG Jian, WANG Juan, LIU Yu. Congenital portosystemic shunts: 2 cases report and review of literature[J]. Chinese Journal of General Practice, 2023, 21(12): 2173-2176. doi: 10.16766/j.cnki.issn.1674-4152.003316

Citation:

XU Jiaxin, DAI Liying, ZHANG Jian, WANG Juan, LIU Yu. Congenital portosystemic shunts: 2 cases report and review of literature[J]. Chinese Journal of General Practice, 2023, 21(12): 2173-2176. doi: 10.16766/j.cnki.issn.1674-4152.003316

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Congenital portosystemic shunts: 2 cases report and review of literature

doi: 10.16766/j.cnki.issn.1674-4152.003316

XU Jiaxin¹
, DAI Liying^{1
,
,}
, ZHANG Jian¹
, WANG Juan²
, LIU Yu²

1.
Department of Neonatology, Anhui Medical University /Anhui Children's Hospital, Hefei, Anhui 230000, China

Funds:

Z155080000004

AHWJ2022b087

Received Date: 2023-06-08
Available Online: 2024-01-29

Abstract

Abstract

To increase clinicians' awareness of congenital portosystemic shunts, pay attention to the details of the child's medical history, achieve early detection and develop individualized treatment plans. Retrospective analysis of clinical data of 2 cases of CPSS in children seen and treated at Anhui Children's Hospital in the past 10 years. Then we systematically searched relevant studies in Chinese and English literature between January 1, 2010 and December 31, 2022 in databases of China Knowledge Network, Wanfang database, Vipshop database, PubMed, GeenMedical, Web of Science using congenital portosystemic shunts, Abernethy syndrome, infants, case report as the keywords.After removing the duplicates and those with incomplete data, we conducted a review of 10 studies with 118 cases. Our analysis of the clinical manifestations, diagnosis and treatment of these cases may help to improve clinicians' understanding of congenital portosystemic shunts and their ability to diagnose and manage the condition.
- Congenital portosystemic shunts,
- Infants,
- Abernethy syndrome,
- Spontaneous closure,
- Literature review

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References(22)

References

[1]	WANG Y, YAN Y N, YANG Z J, et al. Prenatal diagnosis of congenital portosystemic shunt: a single-center study[J]. J Obstet Gynaecol Res, 2020, 46(10): 1988-1993. doi: 10.1111/jog.14403
[2]	季敏, 吴先胜, 龚英, 等. 并发消化道出血的先天性门体分流畸形8例影像学特征病例系列报告[J]. 中国循证儿科杂志, 2017, 12(5): 357-361. JI M, WU X S, GONG Y, et al. Imaging features of 8 cases of congenital portosystemic shunt with gastrointestinal hemorrhage: Case series report[J]. Chinese Journal of Evidence-Based Pediatrics, 2017, 12(5): 357-361.
[3]	向永华, 金科, 徐和平, 等. 儿童先天性门体静脉分流临床及CT表现[J]. 放射学实践, 2020, 35(10): 1320-1323. XIANG Y H, JIN K, XU H P, et al. Clinical and CT findings of congenital portosystemic venous shunts in children[J]. Radiologic Practice, 2020, 35(10): 1320-1323.
[4]	肖云彬, 曾云红, 肖政辉, 等. 先天性门体静脉分流相关性肺动脉高压5例临床分析[J]. 临床儿科杂志, 2019, 37(12): 946-949. XIAO Y B, ZENG Y H, XIAO Z H, et al. Clinical analysis of pulmonary arterial hypertension associated with congenital portosystemic shunt in children[J]. Journal of Clinical Pediatrics, 2019, 37(12): 946-949.
[5]	谢恩萍, 张国庆, 步军. 新生儿先天性门体静脉分流合并髂动脉-脐静脉瘘一例报告并文献复习[J]. 中华新生儿科杂志(中英文), 2017, 32(4): 287-290. XIE E P, ZHANG G Q, BU J, et al. Neonatal congenital portosystemic shunt complicated with iliac artery-umbilical vein fistula: a case report and literature review[J]. Chinese Journal of Neonatology, 2017, 32(4): 287-290.
[6]	XU S H, ZHANG P, HU L Y, et al. Case Report: clinical features of congenital portosystemic shunts in the neonatal period[J]. Front Pediatr, 2021, 9: 778791. DOI: 10.3389/fped.2021.778791.
[7]	DIPAOLA F, TROUT A T, WALTHER A E, et al. Congenital portosystemic shunts in children: associations, complications, and outcomes[J]. Dig Dis Sci, 2020, 65(4): 1239-1251. doi: 10.1007/s10620-019-05834-w
[8]	GONG Y, ZHU H, CHEN J, et al. Congenital portosystemic shunts with and without gastrointestinal bleeding-case series[J]. Pediatr Radiol, 2015, 45(13): 1964-1971. doi: 10.1007/s00247-015-3417-6
[9]	KIM M J, KO J S, SEO J K, et al. Clinical features of congenital portosystemic shunt in children[J]. Eur J Pediatr, 2012, 171(2): 395-400. doi: 10.1007/s00431-011-1564-9
[10]	PEČEK J, FISTER P, HOMAN M. Abernethy syndrome in Slovenian children: five case reports and review of literature[J]. World J Gastroenterol, 2020, 26(37): 5731-5744. doi: 10.3748/wjg.v26.i37.5731
[11]	BLANC T, GUERIN F, FRANCHI-ABELLA S, et al. Congenital portosystemic shunts in children: a new anatomical classification correlated with surgical strategy[J]. Ann Surg, 2014, 260(1): 188-198. doi: 10.1097/SLA.0000000000000266
[12]	FRANCHI-ABELLA S, GONZALES E, ACKERMANN O, et al. Congenital portosystemic shunts: diagnosis and treatment[J]. Abdom Radiol (NY), 2018, 43(8): 2023-2036. doi: 10.1007/s00261-018-1619-8
[13]	PAPAMICHAILl M, PIZANIAS M, HEATON N. Congenital portosystemic venous shunt[J]. Eur J Pediatr, 2018, 177(3): 285-294. doi: 10.1007/s00431-017-3058-x
[14]	SANADA Y, MIZUTA K. Congenital absence of the portal vein: translated version[J]. J Hepatobiliary Pancreat Sci, 2018, 25(8): 359-369. doi: 10.1002/jhbp.572
[15]	陈骊珠, 张墨, 马巍, 等. 蛋白质组学技术在产前诊断生物标志物筛查中的研究进展[J]. 中华全科医学, 2018, 16(3): 461-464. doi: 10.16766/j.cnki.issn.1674-4152.000128 CHEN L Z, ZHANG M, MA W, et al. The main advances in the application of proteomics in prenatal diagnosis[J]. Chinese Journal of General Practice, 2018, 16(3): 461-464. doi: 10.16766/j.cnki.issn.1674-4152.000128
[16]	PONCE-DORREGO M D, HERNÁNDEZ-CABRERO T, GARZÓN-MOLL G. Endovascular treatment of congenital portosystemic shunt: a single-center prospective study[J]. Pediatr Gastroenterol Hepatol Nutr, 2022, 25(2): 147-162. doi: 10.5223/pghn.2022.25.2.147
[17]	XIAO Y B, LI W F, DENG X C, et al. Ligation of patent ductus venosus in a child with pulmonary arterial hypertension and hypersplenism: a case report[J]. Medicine (Baltimore), 2020, 99(34): e21849. DOI: 10.1097/MD.0000000000021849.
[18]	MCLIN V A, FRANCHI ABELLA S, DEBRAY D, et al. Congenital portosystemic shunts: current diagnosis and management[J]. J Pediatr Gastroenterol Nutr, 2019, 68(5): 615-622. doi: 10.1097/MPG.0000000000002263
[19]	赵璐, 吴琳. 儿童先天性门-体分流的诊断和治疗[J]. 中华小儿外科杂志, 2020, 41(1): 93-96. ZHAO L, WU L. Diagnosis and management of congenital portosystemic shunts in children[J]. Chinese Journal of Pediatric Surgery, 2020, 41(1): 93-96.
[20]	LAVERDURE N, LALLIER M, DUBOIS J, et al. Congenital absence of the portal vein: define the portosystemic shunt, avoid liver transplantation[J]. Can Liver J, 2021, 4(3): 322-327. doi: 10.3138/canlivj-2020-0011
[21]	YAN X Y, ZHANG P P, QI Z H, et al. Prenatal diagnosis of intrahepatic congenital portosystemic shunt[J]. J Pediatr, 2022, 251: 212-214. doi: 10.1016/j.jpeds.2022.08.028
[22]	JIMENEZ-GOMEZ J, GÜIZZO J R, BETANCOURTH ALVARENGA J, et al. Correlation of prenatal and postnatal diagnosis in umbilical-portal-systemic venous shunts[J]. Eur J Pediatr Surg, 2023, 33(1): 90-95. doi: 10.1055/s-0042-1760379

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Congenital portosystemic shunts: 2 cases report and review of literature

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